The last fifty years have witnessed dramatic changes in the world of congenital heart disease; innovative cardiac surgeries, noninvasive imaging, and intensive care have all resulted in the successful survival of the majority of babies born with congenital heart disease.
Now, there are approximately one million adults in North America with congenital heart disease, some of whom have had prior surgery and others who were surprised to learn as adults that they were born with heart disease. Although there are now more adults than children with congenital heart disease, the medical community has been ill-prepared to deal with their complex problems. The American College of Cardiology/ American Heart Association have recently recognized the importance of this patient population by publishing guidelines to help medical practitioners manage some of their problems.
The books in the AHA Clinical Series, of which Adult Congenital Heart Disease is included, focus on high-interest, cuttingedge topics in cardiovascular medicine. The aim of this book is to offer further practical advice to physicians about common congenital anomalies and associated complications seen frequently in practice. Eeach chapter of this book begins with a common clinical scenario related to each anomaly. This is followed by a description of the anatomy, features of the clinical diagnosis, a discussion of the imaging modalities, and appropriate treatment strategies. Each chapter then concludes with a discussion about the treatment used for each case and the outcome that resulted. Separate chapters on arrhythmias and imaging are also included.
The authors are an international group of experts in their field, and their contributions are very much appreciated. This book series is a critical tool that supports the AHA mission of promoting healthy behavior and improved care of patients. The readers will benefit from the wealth of clinical experience included herein.
Key Features
- Guides practicing physicians in the practical aspects of how to diagnose and treat patients with congenital heart disease
- Reviews the most common congenital cardiac anomalies seen in practice
- Focuses on both clinical evaluation and diagnostic imaging modalities as well as practical management issues, as well as when to refer patients to tertiary care centres
- Each chapter is preceded by a case study to exemplify the issues which may be challenging in practical management
Contents
1 Secundum atrial septal defect
- Embryology and anatomy
- Pathophysiology
- Natural history
- Diagnosis
- Treatment
- Patient follow-up
2 Atrioventricular septal defects
- Case #1
- Case #2
- Case discussion
- Partial AVSD
- Associated anomalies
- Complete atrioventricular septal defect
- Patient follow-up
3 Pulmonary stenosis / right ventricular outflow tract obstruction
- Introduction
- Valvular pulmonary stenosis
- Subvalvular pulmonary stenosis
- Supravalvular pulmonary stenosis
- Case
- Summary
4 Ventricular septal defect
- Anatomy and pathophysiology
- Practical approach to VSD in adults
- Indication for intervention
- Prognosis
- Conclusion
- Outcome of case
5 Pulmonary arterial hypertension in Eisenmenger Syndrome
- The pathophysiology and genetics of PAH in ES
- The evaluation of PAH in ES
- Managing ES
- Disease-targeting therapies
- Case study
6 Congenitally corrected transposition of the great arteries
- Definition
- Terminology
- Incidence
- Presentation
- Assessment and investigations
- Management
- Medical management issues
- Case study
7 Left ventricular outflow tract obstruction
- General considerations
- Valvular stenosis
- Subvalvular aortic stenosis
- Supravalvular stenosis
- Case conclusion
8 Coarctation of the aorta and aortic disease
- Introduction
- Aortic embryology and development
- Coarctation of the aorta
- Aortopathy
- Case summary
9 Transposition of the great arteries after a Mustard atrial switch procedure
- Background
- Recommendation for follow-up in clinical practice
- Case study
- Conclusion
10 Tetralogy of Fallot
- Introduction
- Anatomy
- Surgical repair
- Long-term complications after surgical repair
- Management of late problems after surgical repair
- Prevention of late problems after surgical repair
- Case study
- Synopsis
11 Single ventricle physiology
- Introduction
- Incidence
- Etiology
- Key components of morphology
- Initial presentation in childhood
- Early palliative procedures
- Subtypes of single ventricle circulations
- Presentation in adulthood
- Long-term outcome in adulthood
- Long-term implications of a Fontan circulation
- Case study
12 Ebstein’s anomaly
- Background
- Pathology, genetics, and classification
- Clinical features
- Associated cardiac lesions
- Diagnosis
- Management
- Catheter ablation and arrhythmia intervention
- Surgical indications and options
- Postoperative findings
- Prognosis
- Conclusions
- Case study
13 Imaging in adult congenital heart disease
- Imaging modalities
- Specific congenital cardiac lesions
- Case outcome
14 The chest x-ray in congenital heart disease
- The bones
- Extrapulmonary soft tissue densities
- The atria
15 Arrhythmias in congenital heart disease
- Introduction
- Treatment of existing arrhythmias
- Risk of sudden death due to arrhythmias
- Prevention of arrhythmias
- Case study
16 Pregnancy and contraception
- Introduction
- Global risk assessment
- High-risk lesions which may preclude pregnancy
- Pregnancy and the woman with congenital heart disease: a lesion-specific approach
- Pregnancy and the woman with congenital heart disease: additional considerations
- Management of labor and delivery
- Contraception
- Case study recommendations
Index
Book Details
- Hardcover: 292 pages
- Publisher: Wiley-Blackwell; 1 edition (May 26, 2009)
- Language: English
- ISBN-10: 1405178205
- ISBN-13: 978-1405178204
List Price: $131.95